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   <subfield code="a">Surgery for tetralogy of Fallot at less than six months of age. Is palliation &quot;old-fashioned&quot;?</subfield>
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   <subfield code="a">There is still no consensus regarding the most appropriate protocol formanaging symptomatic patients with tetralogy of Fallot (TOF) presentingduring early infancy. From January 1987 to April 1994, 83 patients with TOFwere operated on at less than 6 months of age. Sixty patients (mean age 109+/- 5 days) underwent primary repair and 23 (mean age 72 +/- 10 days)underwent initial palliation with a modified Blalock-Taussig shunt (MBTS)in 22 cases. No strict protocol was used but patients who received initialpalliation had lower weight, smaller pulmonary annulus or had an anomalouscoronary artery. Nineteen of the patients initially palliated underwentrepair at a median of 13 months after palliation. During this interval, thepulmonary annulus size increased from a Z- value of -3.0 +/- 0.4 atpalliation to -1.6 +/- 0.7 at repair (P = 0.06) and the summed diameters ofpulmonary artery branches from -2.2 +/- 0.4 to -1.6 +/- 0.7 (P = 0.2).There were no operative deaths among the repaired patients, but twopatients died early after shunt insertion. Transannular patch was requiredin 58% of the patients regardless of the management protocol. Actuarialsurvival rate and freedom from reoperation at 48 months were 98.0% and77.4% (P = 0.003) and 87.6% and 90.0% in primarily repaired and initiallypalliated patients, respectively. Primary repair of TOF at the time ofpresentation is the preferred approach regardless of age.(ABSTRACTTRUNCATED AT 250 WORDS)</subfield>
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