caa a22 4500 445356944 CHVBK 20180317142903.0 cr unu---uuuuu 170323e20110801xx s 000 0 eng 10.1007/s10072-011-0610-8 doi (NATIONALLICENCE)springer-10.1007/s10072-011-0610-8 Steroid-responsive Hashimoto encephalopathy mimicking Creutzfeldt-Jakob disease [Elektronische Daten] [Domenico Santoro, Irene Colombo, Isabella Ghione, Lorenzo Peverelli, Nereo Bresolin, Monica Sciacco, Alessandro Prelle] Hashimoto's encephalopathy (HE) is a rare neurological disorder with a heterogeneous group of neurological symptoms associated with high titres of anti-thyroid antibodies. Clinical manifestations may include encephalopathic features such as seizures, behavioural and psychiatric manifestations, movement disorders and coma. The objective of this presentation is to describe a patient with this rare and controversial clinical syndrome mimicking Creutzfeldt-Jakob disease, associated with a Hashimoto euthyroid thyroiditis and with a significant response to high dose intravenous prednisone. The responsiveness of this syndrome to steroids suggests that this disorder involves immune pathogenic mechanisms, as previous reviews reported. Springer-Verlag, 2011 Encephalopathy nationallicence Hashimoto nationallicence Anti-thyroid antibodies nationallicence Steroids nationallicence Santoro Domenico Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut Colombo Irene Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut Ghione Isabella Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut Peverelli Lorenzo Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut Bresolin Nereo Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut Sciacco Monica Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut Prelle Alessandro Department of Neurological Sciences Azienda Ospedaliera Fatebenefratelli e Oftalmico, UO Neurologia, Corso di Porta Nuova, 23, 20121, Milan, Italy aut Neurological Sciences Springer Milan 32/4(2011-08-01), 719-722 1590-1874 32:4<719 2011 32 10072 https://doi.org/10.1007/s10072-011-0610-8 text/html Onlinezugriff via DOI 1 research-article jats NATIONALLICENCE 856 40 https://doi.org/10.1007/s10072-011-0610-8 text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Santoro Domenico Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut NATIONALLICENCE 700 1- Colombo Irene Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut NATIONALLICENCE 700 1- Ghione Isabella Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut NATIONALLICENCE 700 1- Peverelli Lorenzo Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut NATIONALLICENCE 700 1- Bresolin Nereo Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut NATIONALLICENCE 700 1- Sciacco Monica Department of Neurological Sciences, IRCCS Foundation Ospedale Maggiore Policlinico, Padiglione Ponti, University of Milan, Via Francesco Sforza 35, 20122, Milan, Italy aut NATIONALLICENCE 700 1- Prelle Alessandro Department of Neurological Sciences Azienda Ospedaliera Fatebenefratelli e Oftalmico, UO Neurologia, Corso di Porta Nuova, 23, 20121, Milan, Italy aut NATIONALLICENCE 773 0- Neurological Sciences Springer Milan 32/4(2011-08-01), 719-722 1590-1874 32:4<719 2011 32 10072 Metadata rights reserved Springer special CC-BY-NC licence nationallicence BK010053 XK010053 XK010000 NATIONALLICENCE NATIONALLICENCE NL-springer