caa a22 4500 445824875 CHVBK 20180317145256.0 cr unu---uuuuu 170323e20110401xx s 000 0 eng 10.1007/s00246-010-9867-6 doi (NATIONALLICENCE)springer-10.1007/s00246-010-9867-6 Pentalogy of Cantrell with a Single-Ventricle Cardiac Defect: Collaborative Management of a Complex Disease [Elektronische Daten] [Amy Marino, Richard Levy, John Berger, Mary Donofrio] We present a case of ectopia cordis with a complex single-ventricle congenital heart defect in association with pentalogy of Cantrell. Management by a skilled multidisciplinary team was critical for patient survival. Early fetal diagnosis and the use of advanced imaging techniques allowed adequate time for planning and identified critical anatomic details. Preserving the heart's natural covering, performing cardiac surgery without cardiopulmonary bypass, and using catheter intervention decreased the risk to the patient. Complete coverage of the defect was achieved using skin generated with tissue expanders. This case illustrates the importance of collaboration when caring for infants with critical, high-risk disease and highlights the increased potential for survival with complex ectopia cordis in the current medical era. Springer Science+Business Media, LLC, 2010 Ectopia cordis nationallicence Congenital heart defects nationallicence Omphaloceles nationallicence Fetal heart nationallicence Prenatal ultrasonography nationallicence Cardiac surgical procedure nationallicence Marino Amy Division of Cardiology, Children's National Medical Center, Washington, DC, USA aut Levy Richard Division of Anesthesiology and Pain Medicine, Children's National Medical Center, Washington, DC, USA aut Berger John Division of Cardiology, Children's National Medical Center, Washington, DC, USA aut Donofrio Mary Division of Cardiology, Children's National Medical Center, Washington, DC, USA aut Pediatric Cardiology Springer-Verlag 32/4(2011-04-01), 498-502 0172-0643 32:4<498 2011 32 246 https://doi.org/10.1007/s00246-010-9867-6 text/html Onlinezugriff via DOI 1 research-article jats NATIONALLICENCE 856 40 https://doi.org/10.1007/s00246-010-9867-6 text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Marino Amy Division of Cardiology, Children's National Medical Center, Washington, DC, USA aut NATIONALLICENCE 700 1- Levy Richard Division of Anesthesiology and Pain Medicine, Children's National Medical Center, Washington, DC, USA aut NATIONALLICENCE 700 1- Berger John Division of Cardiology, Children's National Medical Center, Washington, DC, USA aut NATIONALLICENCE 700 1- Donofrio Mary Division of Cardiology, Children's National Medical Center, Washington, DC, USA aut NATIONALLICENCE 773 0- Pediatric Cardiology Springer-Verlag 32/4(2011-04-01), 498-502 0172-0643 32:4<498 2011 32 246 Metadata rights reserved Springer special CC-BY-NC licence nationallicence BK010053 XK010053 XK010000 NATIONALLICENCE NATIONALLICENCE NL-springer