caa a22 4500 445833580 CHVBK 20180317145323.0 cr unu---uuuuu 170323e20110701xx s 000 0 eng 10.1007/s00586-010-1458-y doi (NATIONALLICENCE)springer-10.1007/s00586-010-1458-y Lumbopelvic stabilization with external fixator in a patient with lumbosacral agenesis [Elektronische Daten] [Jacques Griffet, Julien Leroux, Toni El Hayek] A case of caudal regression syndrome in which rehabilitation was obtained by lumbopelvic distraction and stabilization with external fixation Orthofix® is presented. The objective of the study is to describe the benefit of spine external fixator in caudal regression syndrome. Caudal regression syndrome is a rare and sporadic neural defect of distal spinal segments affecting the development of the spinal cord. It is characterized by vertebropelvic instability and essentially manifests as neurological deficit in the lower limbs and absence of bladder and bowel control. Pluridisciplinary management of this affection is complex. The clinical presentation and treatment of caudal regression syndromes are reviewed. A case of a boy for whom physical rehabilitation was obtained with external fixation Orthofix® is presented. Lumbopelvic stabilization was performed with autograft and allograft bone. A spine distraction was performed with external fixation with pedicular screws in L1 and L2 and in the pelvis bone. An elongation of 19mm was obtained in 35days. The external fixator was removed after 4months and a spine cast was applied during 8months. This treatment resulted in lumbopelvic nonunion of very low mobility. Lumbopelvic stability and the disappearance of pain were achieved. Sitting position was stable without hand support. At 14years of follow-up, his condition is stable with possible deambulation at home with crutches. Lumbopelvic arthrodesis in caudal regression syndrome is difficult to obtain. The use of spine external fixator, however, allows trunk elongation and can achieve a stable sitting and upright position. Springer-Verlag, 2010 Lumbosacral agenesia nationallicence Caudal regression nationallicence Lumbopelvic arthrodesis nationallicence External fixator nationallicence Griffet Jacques Department of Paediatric Orthopedic Surgery, University Hospital of Archet, 151 Road of St Antoine de Ginestière, BP 3079, 06202, Nice, France aut Leroux Julien Department of Paediatric Orthopedic Surgery, University Hospital of Archet, 151 Road of St Antoine de Ginestière, BP 3079, 06202, Nice, France aut El Hayek Toni Department of Paediatric Orthopedic Surgery, University Hospital of Archet, 151 Road of St Antoine de Ginestière, BP 3079, 06202, Nice, France aut European Spine Journal Springer-Verlag 20(2011-07-01), 161-165 0940-6719 20<161 2011 20 586 https://doi.org/10.1007/s00586-010-1458-y text/html Onlinezugriff via DOI 1 research-article jats NATIONALLICENCE 856 40 https://doi.org/10.1007/s00586-010-1458-y text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Griffet Jacques Department of Paediatric Orthopedic Surgery, University Hospital of Archet, 151 Road of St Antoine de Ginestière, BP 3079, 06202, Nice, France aut NATIONALLICENCE 700 1- Leroux Julien Department of Paediatric Orthopedic Surgery, University Hospital of Archet, 151 Road of St Antoine de Ginestière, BP 3079, 06202, Nice, France aut NATIONALLICENCE 700 1- El Hayek Toni Department of Paediatric Orthopedic Surgery, University Hospital of Archet, 151 Road of St Antoine de Ginestière, BP 3079, 06202, Nice, France aut NATIONALLICENCE 773 0- European Spine Journal Springer-Verlag 20(2011-07-01), 161-165 0940-6719 20<161 2011 20 586 Metadata rights reserved Springer special CC-BY-NC licence nationallicence BK010053 XK010053 XK010000 NATIONALLICENCE NATIONALLICENCE NL-springer