caa a22 4500 463180208 CHVBK 20180406164836.0 cr unu---uuuuu 170326e20071001xx s 000 0 eng 10.1007/s00381-007-0364-z doi (NATIONALLICENCE)springer-10.1007/s00381-007-0364-z Proteus syndrome with syringohydromyelia and arachnoid cyst [Elektronische Daten] [Yonca Anik, Ihsan Anik, Erdem Gonullu, Nagihan Inan, Ali Demirci] Introduction: Proteus syndrome (PS) is a rarely seen, sporadic disorder with a wide range of abnormalities including asymmetrical overgrowth, skin lesions, dysregulated adipose tissue, and vascular malformations. Brain and spinal malformations are extremely rare; syringohydromyelia and arachnoid cyst have not been reported previously. Materials and methods: We present a 5-year-old girl with PS having severe central nervous system (CNS) abnormalities demonstrated by magnetic resonance imaging (MRI) including craniocutaneous lipomatosis, hemimegalencephaly, arachnoid cyst, and syringohydromyelia. Springer-Verlag, 2007 Proteus syndrome nationallicence Syringohydromyelia nationallicence Arachnoid cyst nationallicence Hemimegalencephaly nationallicence Magnetic resonance imaging nationallicence Anik Yonca School of Medicine, Department of Radiology, University of Kocaeli, 41380, Umuttepe, Kocaeli, Turkey aut Anik Ihsan School of Medicine, Department of Neurosurgery, University of Kocaeli, Umuttepe, Kocaeli, Turkey aut Gonullu Erdem School of Medicine, Department of Pediatry, University of Kocaeli, Umuttepe, Kocaeli, Turkey aut Inan Nagihan School of Medicine, Department of Radiology, University of Kocaeli, 41380, Umuttepe, Kocaeli, Turkey aut Demirci Ali School of Medicine, Department of Radiology, University of Kocaeli, 41380, Umuttepe, Kocaeli, Turkey aut Child's Nervous System Springer-Verlag 23/10(2007-10-01), 1199-1202 0256-7040 23:10<1199 2007 23 381 https://doi.org/10.1007/s00381-007-0364-z text/html Onlinezugriff via DOI 1 research-article jats NATIONALLICENCE 856 40 https://doi.org/10.1007/s00381-007-0364-z text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Anik Yonca School of Medicine, Department of Radiology, University of Kocaeli, 41380, Umuttepe, Kocaeli, Turkey aut NATIONALLICENCE 700 1- Anik Ihsan School of Medicine, Department of Neurosurgery, University of Kocaeli, Umuttepe, Kocaeli, Turkey aut NATIONALLICENCE 700 1- Gonullu Erdem School of Medicine, Department of Pediatry, University of Kocaeli, Umuttepe, Kocaeli, Turkey aut NATIONALLICENCE 700 1- Inan Nagihan School of Medicine, Department of Radiology, University of Kocaeli, 41380, Umuttepe, Kocaeli, Turkey aut NATIONALLICENCE 700 1- Demirci Ali School of Medicine, Department of Radiology, University of Kocaeli, 41380, Umuttepe, Kocaeli, Turkey aut NATIONALLICENCE 773 0- Child's Nervous System Springer-Verlag 23/10(2007-10-01), 1199-1202 0256-7040 23:10<1199 2007 23 381 Metadata rights reserved Springer special CC-BY-NC licence nationallicence BK010053 XK010053 XK010000 NATIONALLICENCE NATIONALLICENCE NL-springer