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   <subfield code="a">Chiari I malformation and intra-cranial hypertension:a case-based review</subfield>
   <subfield code="h">[Elektronische Daten]</subfield>
   <subfield code="c">[Senta Kurschel, Richard Maier, Verena Gellner, Hans Eder]</subfield>
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   <subfield code="a">Objective: To present clinical and morphological findings before and after surgery in a child with Chairi I malformation (CMI) and intra-cranial hypertension (IH). The literature is reviewed and pathophysiologic factors are discussed. Clinical presentation: A 13-year-old obese boy with a 3-week history of headaches, neck pain, torticollis and progressive visual deterioration was admitted. Bi-lateral chronic papilloedema and decrease in visual acuity were found in the presence of a previously diagnosed CMI. Intervention and follow-up: Intra-cranial pressure monitoring demonstrating increased pressure levels was followed by a sub-occipital decompression, C1 laminectomy and duroplasty. Post-operatively, the boy improved markedly, the 6months follow-up opthalmological examination demonstrated resolution of papilloedema, but consecutive bi-lateral optic nerve atrophy. Conclusion: IH with progressive visual deterioration represents one of the varying clinical presentations of CMI and may be classified as a secondary form of idiopathic IH. Neuro-ophthalmological examination in all patients with CMI is recommended to identify the real incidence of this presentation. Altered CSF dynamics, venous hypertension and obesity as co-factors may be causative pathophysiologic factors.</subfield>
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   <subfield code="a">Chiari I malformation</subfield>
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   <subfield code="a">Kurschel</subfield>
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   <subfield code="u">Department of Neurosurgery, Medical University, Auenbruggerplatz 29, 8036, Graz, Austria</subfield>
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   <subfield code="t">Child's Nervous System</subfield>
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