caa a22 4500 463210638 CHVBK 20180405153139.0 cr unu---uuuuu 170326e20071101xx s 000 0 eng 10.1007/s00238-007-0163-5 doi (NATIONALLICENCE)springer-10.1007/s00238-007-0163-5 Evaluation of the outcome of treatment of facial deformities due to Recklinghausen's disease [Elektronische Daten] [Piotr Wójcicki, Kazimierz Kobus, Mikołaj Kubasik, Ireneusz Siewiera] The aim of the study was to evaluate the outcome of treatment of facial deformities in patients with Recklinghausen's disease. Twenty-nine patients suffering from Recklinghausen's disease were treated at the Hospital of Plastic Surgery in Polanica Zdrój in the years 1990-2005. The age of patients when they were first seen was from 1 to 23years (mean age 11years). Most of the patients were followed up for 1 to 31years and were submitted to surgical treatment only periodically. All the patients had facial lesions, including 14 with tumours within the orbits and eyelids. Altogether, 198 partial or complete resections of neurofibromas and corrective procedures were performed (average 6.8 operations per one patient). Nodules on the head, eyelids, cheeks and nose were most commonly resected. Reduction in the tumour mass resulted in improvement of facial symmetry. The resections were often repeated several times in the same area with additional resections in other body areas. Histopathological examinations revealed plexiform neurofibroma in seven cases, while malignant carcinoma was not diagnosed in any of the cases. Three patients developed mild complications (1.5%). Facial neurofibromas occurring in the course of von Recklinghausen's disease require surgical treatment, which is often multi-stage because of benign but progressive proliferation of tumours. Systematic reduction in tumour mass may decrease the risk of malignant transformation. Springer-Verlag, 2007 Von Recklinghausen's disease nationallicence Type 1 neurofibromatosis nationallicence NF 1 nationallicence Surgical treatment of facial neurofibromas nationallicence Wójcicki Piotr ul.Wojska Polskiego 23B, 57-320, Polanica Zdrój, Poland aut Kobus Kazimierz University Clinic of Medical Academy, Wrocław, Poland aut Kubasik Mikołaj Department of Plastic Surgery SCM, Polanica Zdrój, Poland aut Siewiera Ireneusz Department of Plastic Surgery SCM, Polanica Zdrój, Poland aut European Journal of Plastic Surgery Springer-Verlag 30/3(2007-11-01), 119-127 0930-343X 30:3<119 2007 30 238 https://doi.org/10.1007/s00238-007-0163-5 text/html Onlinezugriff via DOI 1 research-article jats NATIONALLICENCE 856 40 https://doi.org/10.1007/s00238-007-0163-5 text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Wójcicki Piotr ul.Wojska Polskiego 23B, 57-320, Polanica Zdrój, Poland aut NATIONALLICENCE 700 1- Kobus Kazimierz University Clinic of Medical Academy, Wrocław, Poland aut NATIONALLICENCE 700 1- Kubasik Mikołaj Department of Plastic Surgery SCM, Polanica Zdrój, Poland aut NATIONALLICENCE 700 1- Siewiera Ireneusz Department of Plastic Surgery SCM, Polanica Zdrój, Poland aut NATIONALLICENCE 773 0- European Journal of Plastic Surgery Springer-Verlag 30/3(2007-11-01), 119-127 0930-343X 30:3<119 2007 30 238 Metadata rights reserved Springer special CC-BY-NC licence nationallicence BK010053 XK010053 XK010000 NATIONALLICENCE NATIONALLICENCE NL-springer