caa a22 4500 463210689 CHVBK 20180405153139.0 cr unu---uuuuu 170326e20071101xx s 000 0 eng 10.1007/s00238-007-0161-7 doi (NATIONALLICENCE)springer-10.1007/s00238-007-0161-7 Hand abnormalities in Apert's syndrome: surgical management [Elektronische Daten] [B. Salazard, P. Galinier, P. Samson, D. Casanova, G. Magalon] Apert's syndrome is the most common of the acrocephalosyndactylies with complex malformations of the hands. Treatment of the Apert hand is complex, and numerous procedures are required. The aim of this study is to propose a strategy for hand management. Sixteen Apert's syndrome hands were submitted to early surgery, which included opening of the first web, separation of the fingers, realigninment of the thumb, and correction of the clinodactylies. We performed an average of six operations per child. Treatment of the first web depended on the classification of Upton: For the severe stages, we used a dorsal hand flap. Radical clinodactyly was treated by osteotomy of the delta phalanx and Z-plasty. We treated nine hands with four fingers and seven hands with five fingers. There was always bilateral opposition and symphalangism excluding the fifth finger. All of the children have a rudimentary but functional pinch grip. Revision of the webs was necessary in 16% of the cases. The Apert hand requires early and specialized treatment that aims to provide a functional hand before 2 or 3years, with the least surgical complications. The functional prognosis is adversely affected by symphalangism. Springer-Verlag, 2007 Apert's syndrome nationallicence Complex syndactyly nationallicence Dorsal flap nationallicence Salazard B. Department of Paediatric Plastic and Reconstructive Surgery, Timone Children's Hospital, Marseille, France aut Galinier P. Department of Paediatric Plastic and Reconstructive Surgery, Children's Hospital, Toulouse, France aut Samson P. Department of Paediatric Plastic and Reconstructive Surgery, Timone Children's Hospital, Marseille, France aut Casanova D. Department of Paediatric Plastic and Reconstructive Surgery, Timone Children's Hospital, Marseille, France aut Magalon G. Department of Paediatric Plastic and Reconstructive Surgery, Timone Children's Hospital, Marseille, France aut European Journal of Plastic Surgery Springer-Verlag 30/3(2007-11-01), 107-112 0930-343X 30:3<107 2007 30 238 https://doi.org/10.1007/s00238-007-0161-7 text/html Onlinezugriff via DOI 1 research-article jats NATIONALLICENCE 856 40 https://doi.org/10.1007/s00238-007-0161-7 text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Salazard B. Department of Paediatric Plastic and Reconstructive Surgery, Timone Children's Hospital, Marseille, France aut NATIONALLICENCE 700 1- Galinier P. Department of Paediatric Plastic and Reconstructive Surgery, Children's Hospital, Toulouse, France aut NATIONALLICENCE 700 1- Samson P. Department of Paediatric Plastic and Reconstructive Surgery, Timone Children's Hospital, Marseille, France aut NATIONALLICENCE 700 1- Casanova D. Department of Paediatric Plastic and Reconstructive Surgery, Timone Children's Hospital, Marseille, France aut NATIONALLICENCE 700 1- Magalon G. Department of Paediatric Plastic and Reconstructive Surgery, Timone Children's Hospital, Marseille, France aut NATIONALLICENCE 773 0- European Journal of Plastic Surgery Springer-Verlag 30/3(2007-11-01), 107-112 0930-343X 30:3<107 2007 30 238 Metadata rights reserved Springer special CC-BY-NC licence nationallicence BK010053 XK010053 XK010000 NATIONALLICENCE NATIONALLICENCE NL-springer