caa a22 4500 465772234 CHVBK 20180323111932.0 cr unu---uuuuu 170327e19900501xx s 000 0 eng 10.1007/BF00179665 doi (NATIONALLICENCE)springer-10.1007/BF00179665 The prune belly syndrome in a female [Elektronische Daten] A case report and review of the literature [R. Shaw, J. Smyth, K. Pringle] Prune belly syndrome is an extremely rare congenital condition in both sexes, particularly in females, with less than 50 cases having been reported; by comparison, the condition is at most uncommon in males. There has been much debate over the pathogenesis of the syndrome, in particular between two main theories. The first implicates a failure of mesodermal cell migration as the primary cause, whereas the second pinpoints urinary distention as the initial event. We describe a case of prune belly syndrome in a female that backs up the second of these theories. The features and the alternative theories as to the aetiology of this syndrome are reviewed, along with an explanation for the marked sex difference. Springer-Verlag, 1990 Prune belly syndrome nationallicence Urinary tract nationallicence Obstruction nationallicence Obstructive uropathy nationallicence Shaw R. Departments of Paediatrics and Surgery, Willington Hospital, Wellington, New Zealand aut Smyth J. Departments of Paediatrics and Surgery, Willington Hospital, Wellington, New Zealand aut Pringle K. Departments of Paediatrics and Surgery, Willington Hospital, Wellington, New Zealand aut Pediatric Surgery International Springer-Verlag 5/3(1990-05-01), 202-207 0179-0358 5:3<202 1990 5 383 https://doi.org/10.1007/BF00179665 text/html Onlinezugriff via DOI 1 research-article jats NATIONALLICENCE 856 40 https://doi.org/10.1007/BF00179665 text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Shaw R. Departments of Paediatrics and Surgery, Willington Hospital, Wellington, New Zealand aut NATIONALLICENCE 700 1- Smyth J. Departments of Paediatrics and Surgery, Willington Hospital, Wellington, New Zealand aut NATIONALLICENCE 700 1- Pringle K. Departments of Paediatrics and Surgery, Willington Hospital, Wellington, New Zealand aut NATIONALLICENCE 773 0- Pediatric Surgery International Springer-Verlag 5/3(1990-05-01), 202-207 0179-0358 5:3<202 1990 5 383 Metadata rights reserved Springer special CC-BY-NC licence nationallicence BK010053 XK010053 XK010000 NATIONALLICENCE NATIONALLICENCE NL-springer