caa a22 4500 469043865 CHVBK 20180323132818.0 cr unu---uuuuu 170328e19920101xx s 000 0 eng 10.1007/BF01800355 doi (NATIONALLICENCE)springer-10.1007/BF01800355 A synopsis of the unconjugated acidic transamination metabolites of phenylalanine in phenylketonuria [Elektronische Daten] [U. Langenbeck, A. Behbehani, A. Mench-Hoinowski] Summary: We present blood and urine levels of unconjugatedo-hydroxyphenylacetic, phenyllactic and phenylpyruvic acids in 61 children (2 years of age and above) and juveniles with phenylketonuria on or partially off diet. The samples were obtained during 185 scheduled outpatient visits and have been analysed with gas chromatographic methods. The compiled data define reference ranges of phenylalanine transamination capacity and of renal transport of metabolites which may be of value in further studies on the pathogenesis of phenylketonuria. SSIEM and Kluwer Academic Publishers, 1992 Langenbeck U. Institute of Human Genetics, University of Göttingen, D-3400, Göttingen, Germany aut Behbehani A. formerly Children's Hospital, University of Göttingen, D-3400, Göttingen, Germany aut Mench-Hoinowski A. Institute of Human Genetics, University of Göttingen, D-3400, Göttingen, Germany aut Journal of Inherited Metabolic Disease Kluwer Academic Publishers 15/1(1992-01-01), 136-144 0141-8955 15:1<136 1992 15 10545 https://doi.org/10.1007/BF01800355 text/html Onlinezugriff via DOI 1 research-article jats NATIONALLICENCE 856 40 https://doi.org/10.1007/BF01800355 text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Langenbeck U. Institute of Human Genetics, University of Göttingen, D-3400, Göttingen, Germany aut NATIONALLICENCE 700 1- Behbehani A. formerly Children's Hospital, University of Göttingen, D-3400, Göttingen, Germany aut NATIONALLICENCE 700 1- Mench-Hoinowski A. Institute of Human Genetics, University of Göttingen, D-3400, Göttingen, Germany aut NATIONALLICENCE 773 0- Journal of Inherited Metabolic Disease Kluwer Academic Publishers 15/1(1992-01-01), 136-144 0141-8955 15:1<136 1992 15 10545 Metadata rights reserved Springer special CC-BY-NC licence nationallicence BK010053 XK010053 XK010000 NATIONALLICENCE NATIONALLICENCE NL-springer