caa a22 4500 469050640 CHVBK 20180323132829.0 cr unu---uuuuu 170328e19920601xx s 000 0 eng 10.1007/BF02493441 doi (NATIONALLICENCE)springer-10.1007/BF02493441 Dysphagi in Huntington's disease: A 16-year retrospective [Elektronische Daten] [Marion Kagel, Norman Leopold] Degenerative diseases of the basal ganglia are commonly complicated by dysphagia. In 35 patients with Huntington's disease (HD), a hereditary neurodegenerative basal ganglia disease characterized by chorea, dementia, and emotional changes, an extensive battery of clinical and radiologic procedures helped to identify numerous abnormalities of deglutition. The results permitted the classification of our patients with HD into hyperkinetic (HD-h) or rigid-bradykinetic (HD-rb) groups. Although the two groups share multiple abnormalities, statistically significant intergroup differences were observed. Clincial assessmen of the HD-h cohort (30 patients) demonstrated rapid lingual chorea, swallow incoordination repetitive swallows, prolonged laryngeal elevation, inability to stop respiration and frequent eructations. In the HD-rb group (five patients), frequently observed abnormalities included mandibular rigidity, slow lingual chorea, coughing on foods, and choking on liquids. Videofluoroscopic swallowing studies (VFSS) using a variety of barium-impregnated, foods and liquids confirmed the abnormalities noted on the clinical assessment. Respiratory and laryngeal chorea, pharyngeal space retention, and aspiration were also identified. Numerous compensatory techniques introduced during videofluoroscopy benefited all patients. Springer-Verlag New York Inc, 1992 Huntington's disease nationallicence Chorea nationallicence Rigidity nationallicence Respiration nationallicence Aspiration nationallicence Deglutition nationallicence Deglution disorders nationallicence Kagel Marion Department of Medicine, Divisions of Speech/Language Pathology, Crozer-Chester, Medical Center, Upland, POB #2, Suite 222, 19013, Chester, PA, USA aut Leopold Norman Department of Neurology, Hahnemann University School of Medicine, Philadelphia, Pennsylvania, USA aut Dysphagia Springer-Verlag 7/2(1992-06-01), 106-114 0179-051X 7:2<106 1992 7 455 https://doi.org/10.1007/BF02493441 text/html Onlinezugriff via DOI 1 research-article jats NATIONALLICENCE 856 40 https://doi.org/10.1007/BF02493441 text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Kagel Marion Department of Medicine, Divisions of Speech/Language Pathology, Crozer-Chester, Medical Center, Upland, POB #2, Suite 222, 19013, Chester, PA, USA aut NATIONALLICENCE 700 1- Leopold Norman Department of Neurology, Hahnemann University School of Medicine, Philadelphia, Pennsylvania, USA aut NATIONALLICENCE 773 0- Dysphagia Springer-Verlag 7/2(1992-06-01), 106-114 0179-051X 7:2<106 1992 7 455 Metadata rights reserved Springer special CC-BY-NC licence nationallicence BK010053 XK010053 XK010000 NATIONALLICENCE NATIONALLICENCE NL-springer