caa a22 4500 475752856 CHVBK 20180406123529.0 cr unu---uuuuu 170329e20000301xx s 000 0 eng 10.1007/s005950050057 doi (NATIONALLICENCE)springer-10.1007/s005950050057 Congenital hepatoportal arteriovenous fistula: Report of a case [Elektronische Daten] [Sandeep Agarwala, Hemonta Dutta, Veereshwar Bhatnagar, Manpreet Gulathi, Sashi Paul, DilipKumar Mitra] Fistulae between the hepatic artery and portal vein, known as hepatoportal arteriovenous fistula (HPAVF), most commonly occur secondary to trauma or malignancy. Congenital HPAVF is an extremely rare anomaly and only 11 pediatric cases have been documented to date HPAVF causes portal hypertension with the reversal of flow in the portal circulation, leading to hyperemia and congestion of the bowel, causing severe ascites, gastrointestinal bleeding, anemia, and malabsorption. The diagnosis is first made by Doppler sonography, then confirmed by angiography. HPAVF is most effectively treated by performing either ligation of the hepatic artery or percutaneous transcatheter embolization. We describe herein the case of an 8-month-old boy diagnosed to have congenital HPAVF by duplex Doppler sonography and confirmed by digital subtraction angiography, who was successfully managed by percutaneous transcatheter embolization of the feeding right hepatic artery. A review of the previously reported 11 cases of infants with this unusual anomaly, examining presentation, management, and outcome, is also presented. Springer-Verlag, 2000 congenital hepatoportal arteriovenous fistula nationallicence transcatheter embolization nationallicence Agarwala Sandeep Department of Paediatric Surgery, All India Institute of Medical Sciences, 110029, New Delhi, India aut Dutta Hemonta Department of Paediatric Surgery, All India Institute of Medical Sciences, 110029, New Delhi, India aut Bhatnagar Veereshwar Department of Paediatric Surgery, All India Institute of Medical Sciences, 110029, New Delhi, India aut Gulathi Manpreet Department of Radiodiagnosis, All India Institute of Medical Sciences, 110029, New Delhi, India aut Paul Sashi Department of Radiodiagnosis, All India Institute of Medical Sciences, 110029, New Delhi, India aut Mitra DilipKumar Department of Paediatric Surgery, All India Institute of Medical Sciences, 110029, New Delhi, India aut Surgery Today Springer-Verlag 30/3(2000-03-01), 268-271 0941-1291 30:3<268 2000 30 595 https://doi.org/10.1007/s005950050057 text/html Onlinezugriff via DOI 1 research-article jats NATIONALLICENCE 856 40 https://doi.org/10.1007/s005950050057 text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Agarwala Sandeep Department of Paediatric Surgery, All India Institute of Medical Sciences, 110029, New Delhi, India aut NATIONALLICENCE 700 1- Dutta Hemonta Department of Paediatric Surgery, All India Institute of Medical Sciences, 110029, New Delhi, India aut NATIONALLICENCE 700 1- Bhatnagar Veereshwar Department of Paediatric Surgery, All India Institute of Medical Sciences, 110029, New Delhi, India aut NATIONALLICENCE 700 1- Gulathi Manpreet Department of Radiodiagnosis, All India Institute of Medical Sciences, 110029, New Delhi, India aut NATIONALLICENCE 700 1- Paul Sashi Department of Radiodiagnosis, All India Institute of Medical Sciences, 110029, New Delhi, India aut NATIONALLICENCE 700 1- Mitra DilipKumar Department of Paediatric Surgery, All India Institute of Medical Sciences, 110029, New Delhi, India aut NATIONALLICENCE 773 0- Surgery Today Springer-Verlag 30/3(2000-03-01), 268-271 0941-1291 30:3<268 2000 30 595 Metadata rights reserved Springer special CC-BY-NC licence nationallicence BK010053 XK010053 XK010000 NATIONALLICENCE NATIONALLICENCE NL-springer