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   <subfield code="a">Disseminated lymphangiomatosis presenting with massive chylothorax</subfield>
   <subfield code="h">[Elektronische Daten]</subfield>
   <subfield code="c">[O. Konez, P. K. Vyas, M. Goyal]</subfield>
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   <subfield code="a">Background. Lymphangiomatosis is a disease characterized by involvement of various body constituents and can involve the skeletal system, connective tissues, and visceral organs.¶Materials and methods. We present a case of a 9-year-old girl where this entity presented with extensive right-sided chylothorax. Conventional imaging, including skeletal scintigraphy and contrast enhanced CT of the chest and abdomen, may have underestimated the extent of the disease, as seen on follow-up T2-weighted MR images of the chest and abdomen in our case.¶Results. MRI easily demonstrated additional bone lesions as well as multiple small splenic lesions, which were difficult to appreciate on prior CT examinations.¶Conclusion. We suggest that MRI may be helpful to assess the extent of this disease more accurately.</subfield>
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