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   <subfield code="a">A study of glycogen storage disease with 99Tcm-MIBI gated myocardial perfusion imaging</subfield>
   <subfield code="h">[Elektronische Daten]</subfield>
   <subfield code="c">[L. Wei, J. Gao, X. Liu, J. Huang, X. Li]</subfield>
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   <subfield code="a">Objective: Gated myocardial perfusion imaging (G-MPI) is regularly performed using single-photon emission computed tomography. The objective of this study was to evaluate the clinical value of 99Tcm-methoxyisobutylisonitrile (MIBI) myocardial imaging in glycogen storage disease (GSD). Methods: 99Tcm-MIBI G-MPI was performed in nine patients with clinically proven GSD. QGS quantitative software was used for processing and interpretation. Left ventricular ejection fraction (LVEF), end-diastolic volume (EDV) and end-systolic volume (ESV) were automatically generated. The myocardium was divided into seven segments, 20 sub-segments and a five-point scoring system was used. Results: Seven out of nine cases were abnormal and the positive rate of G-MPI was 77.8%. Sixty-two sub-segments of injured myocardium were detected in 140 sub-segments of seven abnormal patients. One injured segment was observed in one patient (14.3%), two segments were detected in two patients (28.6%) and three or more abnormal segments were observed in four patients (57.1%). Conclusion: 99Tcm-MIBI G-MPI can detect myocardial damage in GSD as a non-invasive method. It plays an important role in the clinic.</subfield>
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   <subfield code="a">Royal Academy of Medicine in Ireland, 2013</subfield>
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   <subfield code="a">Glycogen storage disease</subfield>
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   <subfield code="a">Tomography</subfield>
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   <subfield code="a">Emission computed</subfield>
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   <subfield code="a">Single-photon</subfield>
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   <subfield code="a">MIBI</subfield>
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   <subfield code="a">Wei</subfield>
   <subfield code="D">L.</subfield>
   <subfield code="u">Department of Nuclear Medicine, The Third Affiliated Hospital of Hebei Medical University, 050051, Shijiazhuang, China</subfield>
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   <subfield code="a">Gao</subfield>
   <subfield code="D">J.</subfield>
   <subfield code="u">Department of Nuclear Medicine, The Third Affiliated Hospital of Hebei Medical University, 050051, Shijiazhuang, China</subfield>
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   <subfield code="a">Liu</subfield>
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   <subfield code="u">Department of Nuclear Medicine, The Third Affiliated Hospital of Hebei Medical University, 050051, Shijiazhuang, China</subfield>
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   <subfield code="a">Huang</subfield>
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   <subfield code="u">Department of Nuclear Medicine, The Third Affiliated Hospital of Hebei Medical University, 050051, Shijiazhuang, China</subfield>
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   <subfield code="t">Irish Journal of Medical Science</subfield>
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   <subfield code="g">182/4(2013-12-01), 615-620</subfield>
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