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   <subfield code="a">Sacral chordoma: management of a rare disease in a tertiary hospital</subfield>
   <subfield code="h">[Elektronische Daten]</subfield>
   <subfield code="c">[Gada Housari, Mariana González, Purificación Calero, Rafael Beni, Eduardo Lobo]</subfield>
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   <subfield code="a">Introduction: Chordoma is a rare malignant bone tumor. The outcome depends on the adequate surgical treatment with complete excision of the tumor with microscopic clear margins. Materials and methods: We performed a retrospective review of 13 cases of chordomas operated in our center between 1988 and 2009. Results: All cases were treated with wide excision. Inadequate margins were found in seven patients. There were complications in ten patients and long-term sequels in 11 patients. Nine had recurrence within the first 2years, six of which had inadequate margins. Five had metastatic disease, three of them with inadequate margins. During the follow-up, four patients died. In a posterior review, three patients survive and all of them had clear margins. Conclusions: In our experience, the best treatment is complete excision of the tumor with clear microscopic margins. When this is not possible, local recurrences increase and survival rate decreases.</subfield>
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   <subfield code="a">Federación de Sociedades Españolas de Oncología (FESEO), 2012</subfield>
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   <subfield code="a">Chordoma</subfield>
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   <subfield code="u">Department of General and Digestive Surgery, Hospital Universitario Ramón y Cajal, C/Buenos Aires, 5. 1° 2, 28822, Coslada (Madrid), Spain</subfield>
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