Herlyn-Werner-Wunderlich syndrome: pre- and post-surgical MRI and US findings

Verfasser / Beitragende:
[João Lopes Dias, Renata Jogo]
Ort, Verlag, Jahr:
2015
Enthalten in:
Abdominal Imaging, 40/7(2015-10-01), 2667-2682
Format:
Artikel (online)
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024 7 0 |a 10.1007/s00261-015-0421-0  |2 doi 
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245 0 0 |a Herlyn-Werner-Wunderlich syndrome: pre- and post-surgical MRI and US findings  |h [Elektronische Daten]  |c [João Lopes Dias, Renata Jogo] 
520 3 |a Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare congenital anomaly of the female urogenital tract that associates Müllerian duct anomalies with mesonephric duct anomalies. The triad of uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis characterizes this syndrome. Patients generally present with non-specific symptoms after menarche. Pelvic pain, dysmenorrhea, and palpable mass due to hematocolpos or hematometra are the most common findings. Pyohematocolpos and pyosalpinx may appear as acute complications, while endometriosis and pelvic adhesions constitute potential long-term complications. When a prenatal diagnosis of unilateral renal agenesis in newborn girls is known, a gynecological imaging study should be performed to exclude uterine and vaginal abnormalities. These patients should be followed up to ensure that a timely surgical correction is performed. The diagnosis of HWWS is difficult due to the lack of specific symptoms or findings upon physical examination. An accurate imaging description of these congenital anomalies is crucial to guide patients toward surgical treatment, relieving acute complications, and preserving the normal fertility. The authors provide a pictorial review of the magnetic resonance imaging and ultrasonography findings of the HWWS with correlation to embryological, clinical, and surgical features. 
540 |a Springer Science+Business Media New York, 2015 
690 7 |a Herlyn-Werner-Wunderlich syndrome  |2 nationallicence 
690 7 |a Müllerian duct anomalies  |2 nationallicence 
690 7 |a Mesonephric duct anomalies  |2 nationallicence 
690 7 |a Uterus didelphys  |2 nationallicence 
690 7 |a Hematocolpos  |2 nationallicence 
690 7 |a Renal agenesis  |2 nationallicence 
700 1 |a Lopes Dias  |D João  |u Department of Radiology, Hospital de São José, Centro Hospitalar de Lisboa Central, Lisbon, Portugal  |4 aut 
700 1 |a Jogo  |D Renata  |u Department of Radiology, Hospital de D. Estefânia, Centro Hospitalar de Lisboa Central, Lisbon, Portugal  |4 aut 
773 0 |t Abdominal Imaging  |d Springer US; http://www.springer-ny.com  |g 40/7(2015-10-01), 2667-2682  |x 0942-8925  |q 40:7<2667  |1 2015  |2 40  |o 261 
856 4 0 |u https://doi.org/10.1007/s00261-015-0421-0  |q text/html  |z Onlinezugriff via DOI 
898 |a BK010053  |b XK010053  |c XK010000 
900 7 |a Metadata rights reserved  |b Springer special CC-BY-NC licence  |2 nationallicence 
908 |D 1  |a review-article  |2 jats 
949 |B NATIONALLICENCE  |F NATIONALLICENCE  |b NL-springer 
950 |B NATIONALLICENCE  |P 856  |E 40  |u https://doi.org/10.1007/s00261-015-0421-0  |q text/html  |z Onlinezugriff via DOI 
950 |B NATIONALLICENCE  |P 700  |E 1-  |a Lopes Dias  |D João  |u Department of Radiology, Hospital de São José, Centro Hospitalar de Lisboa Central, Lisbon, Portugal  |4 aut 
950 |B NATIONALLICENCE  |P 700  |E 1-  |a Jogo  |D Renata  |u Department of Radiology, Hospital de D. Estefânia, Centro Hospitalar de Lisboa Central, Lisbon, Portugal  |4 aut 
950 |B NATIONALLICENCE  |P 773  |E 0-  |t Abdominal Imaging  |d Springer US; http://www.springer-ny.com  |g 40/7(2015-10-01), 2667-2682  |x 0942-8925  |q 40:7<2667  |1 2015  |2 40  |o 261