caa a22 4500 605493111 CHVBK 20210128100519.0 cr unu---uuuuu 210128e20151001xx s 000 0 eng 10.1007/s00261-015-0421-0 doi (NATIONALLICENCE)springer-10.1007/s00261-015-0421-0 Herlyn-Werner-Wunderlich syndrome: pre- and post-surgical MRI and US findings [Elektronische Daten] [João Lopes Dias, Renata Jogo] Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare congenital anomaly of the female urogenital tract that associates Müllerian duct anomalies with mesonephric duct anomalies. The triad of uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis characterizes this syndrome. Patients generally present with non-specific symptoms after menarche. Pelvic pain, dysmenorrhea, and palpable mass due to hematocolpos or hematometra are the most common findings. Pyohematocolpos and pyosalpinx may appear as acute complications, while endometriosis and pelvic adhesions constitute potential long-term complications. When a prenatal diagnosis of unilateral renal agenesis in newborn girls is known, a gynecological imaging study should be performed to exclude uterine and vaginal abnormalities. These patients should be followed up to ensure that a timely surgical correction is performed. The diagnosis of HWWS is difficult due to the lack of specific symptoms or findings upon physical examination. An accurate imaging description of these congenital anomalies is crucial to guide patients toward surgical treatment, relieving acute complications, and preserving the normal fertility. The authors provide a pictorial review of the magnetic resonance imaging and ultrasonography findings of the HWWS with correlation to embryological, clinical, and surgical features. Springer Science+Business Media New York, 2015 Herlyn-Werner-Wunderlich syndrome nationallicence Müllerian duct anomalies nationallicence Mesonephric duct anomalies nationallicence Uterus didelphys nationallicence Hematocolpos nationallicence Renal agenesis nationallicence Lopes Dias João Department of Radiology, Hospital de São José, Centro Hospitalar de Lisboa Central, Lisbon, Portugal aut Jogo Renata Department of Radiology, Hospital de D. Estefânia, Centro Hospitalar de Lisboa Central, Lisbon, Portugal aut Abdominal Imaging Springer US; http://www.springer-ny.com 40/7(2015-10-01), 2667-2682 0942-8925 40:7<2667 2015 40 261 https://doi.org/10.1007/s00261-015-0421-0 text/html Onlinezugriff via DOI BK010053 XK010053 XK010000 Metadata rights reserved Springer special CC-BY-NC licence nationallicence 1 review-article jats NATIONALLICENCE NATIONALLICENCE NL-springer NATIONALLICENCE 856 40 https://doi.org/10.1007/s00261-015-0421-0 text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Lopes Dias João Department of Radiology, Hospital de São José, Centro Hospitalar de Lisboa Central, Lisbon, Portugal aut NATIONALLICENCE 700 1- Jogo Renata Department of Radiology, Hospital de D. Estefânia, Centro Hospitalar de Lisboa Central, Lisbon, Portugal aut NATIONALLICENCE 773 0- Abdominal Imaging Springer US; http://www.springer-ny.com 40/7(2015-10-01), 2667-2682 0942-8925 40:7<2667 2015 40 261