caa a22 4500 606184562 CHVBK 20210128100827.0 cr unu---uuuuu 210128e20151201xx s 000 0 eng 10.1007/s00405-014-3371-1 doi (NATIONALLICENCE)springer-10.1007/s00405-014-3371-1 Hearing disorders in Turner's syndrome: a survey from Iran [Elektronische Daten] [Mehdi Bakhshaee, Rahim Vakili, Navid Nourizadeh, Mohsen Rajati, Asma Ahrari, Rahman Movahed] Turner syndrome (TS) is one of the most frequently encountered sex-linked chromosomal abnormalities, occurring in one per 2,000 female births. These patients present with short stature and failure to begin puberty. In this syndrome, there are multiple organ abnormalities, including auditory disorders. TS patients were referred to the ENT clinic by a pediatric endocrinologist. A questionnaire was filled out and the patients went through a complete otologic examination. They were then referred to the audiology clinic to undergo audiologic test battery plus high-frequency pure tone audiometry. From a total of 48 ears examined, 11 (22.9%) had a normal audiometry. Mid-frequency sensorineural hearing loss (SNHL), high-frequency SNHL, combined and mixed hearing loss were diagnosed in 6 (12/5%), 20 (41/7%), 6 (12/5%) and 1 (2/1%) ear, respectively. Tympanogram results showed normal compliance (A, As, Ad) in the majority of cases. B and C patterns were found in a few cases. Speech discrimination score was normal in all patients whereas speech reception threshold was normal in 92% of the ears. Audiometry abnormality especially SNHL is common in TS patients, with the high-frequency pattern being the most frequent. Springer-Verlag Berlin Heidelberg, 2014 Ear nationallicence Turner syndrome nationallicence Hearing loss nationallicence Auditory disorders nationallicence Bakhshaee Mehdi Sinus and Surgical Endoscopic Research Center, Imam Reza Educational Hospital, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut Vakili Rahim Department of Pediatrics, Imam Reza Hospital, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut Nourizadeh Navid Sinus and Surgical Endoscopic Research Center, Imam Reza Educational Hospital, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut Rajati Mohsen Sinus and Surgical Endoscopic Research Center, Imam Reza Educational Hospital, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut Ahrari Asma Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut Movahed Rahman Sinus and Surgical Endoscopic Research Center, Imam Reza Educational Hospital, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut European Archives of Oto-Rhino-Laryngology Springer Berlin Heidelberg 272/12(2015-12-01), 3705-3708 0937-4477 272:12<3705 2015 272 405 https://doi.org/10.1007/s00405-014-3371-1 text/html Onlinezugriff via DOI BK010053 XK010053 XK010000 Metadata rights reserved Springer special CC-BY-NC licence nationallicence 1 research-article jats NATIONALLICENCE NATIONALLICENCE NL-springer NATIONALLICENCE 856 40 https://doi.org/10.1007/s00405-014-3371-1 text/html Onlinezugriff via DOI NATIONALLICENCE 700 1- Bakhshaee Mehdi Sinus and Surgical Endoscopic Research Center, Imam Reza Educational Hospital, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut NATIONALLICENCE 700 1- Vakili Rahim Department of Pediatrics, Imam Reza Hospital, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut NATIONALLICENCE 700 1- Nourizadeh Navid Sinus and Surgical Endoscopic Research Center, Imam Reza Educational Hospital, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut NATIONALLICENCE 700 1- Rajati Mohsen Sinus and Surgical Endoscopic Research Center, Imam Reza Educational Hospital, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut NATIONALLICENCE 700 1- Ahrari Asma Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut NATIONALLICENCE 700 1- Movahed Rahman Sinus and Surgical Endoscopic Research Center, Imam Reza Educational Hospital, Faculty of Medicine, Mashhad University of Medical Sciences, Mashhad, Iran aut NATIONALLICENCE 773 0- European Archives of Oto-Rhino-Laryngology Springer Berlin Heidelberg 272/12(2015-12-01), 3705-3708 0937-4477 272:12<3705 2015 272 405