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   <subfield code="a">Persistent Müllerian Duct Syndrome (PMDS): a Rare Anomaly the General Surgeon Must Know About</subfield>
   <subfield code="h">[Elektronische Daten]</subfield>
   <subfield code="c">[Aditi Agrawal, Raman Kataria]</subfield>
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   <subfield code="a">Persistent Müllerian duct syndrome is a rare condition occasionally encountered in men with normal phenotype but with presence of Müllerian duct structures. In India, owing to neglect and lack of facilities, we encounter this condition in adult males. We encountered on the same day in the operation theatre two phenotypic males aged 40years and 10months who had inguinal hernia on one side along with contralateral undescended testis. Both patients intraoperatively had uterus with fallopian tubes and underwent subtotal hysterectomy with preservation of vas. Repair of inguinal hernia with fixation of the testis in the scrotum was done. Though rare, every surgeon operating upon inguinal hernia or undescended testes or cryptorchidism needs to know about the presence of the uterus in a phenotypic male patient at any age. High degree of suspicion and awareness is needed to diagnose this condition. Early treatment is needed to maintain fertility and to prevent the occurrence of malignancy in remnant müllerian structures.</subfield>
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   <subfield code="a">Association of Surgeons of India, 2014</subfield>
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   <subfield code="a">Persistent Müllerian duct syndrome</subfield>
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   <subfield code="a">Phenotypic male</subfield>
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   <subfield code="a">PMDS : Persistent Müllerian duct syndrome</subfield>
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   <subfield code="a">MIF : Müllerian inhibitory factor</subfield>
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   <subfield code="a">MGD : Mixed gonadal dysgenesis</subfield>
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   <subfield code="a">TTE : Transverse testicular ectopia</subfield>
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   <subfield code="a">Agrawal</subfield>
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   <subfield code="a">Metadata rights reserved</subfield>
   <subfield code="b">Springer special CC-BY-NC licence</subfield>
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